Histidine ammonia-lyase


Histidine ammonia-lyase

protein
Name=histidine ammonia-lyase
caption=


width=
HGNCid=4806
Symbol=HAL
AltSymbols=HIS
EntrezGene=3034
OMIM=609457
RefSeq=NM_002108
UniProt=P42357
PDB=
ECnumber=4.3.1.3
Chromosome=12
Arm=q
Band=22
LocusSupplementaryData=-q24.1

Histidine ammonia-lyase (or histidase) is an enzyme which converts histidine into ammonia and urocanic acid.

Pathology

Mutations in the gene for histidase are associated with histidinemia and urocanic aciduria.

External links

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Look at other dictionaries:

  • histidine ammonia-lyase — his·ti·dine am·mo·nia ly·ase (hisґtĭ dēn ə moґne ə liґās) [EC 4.3.1.3] an enzyme of the lyase class that catalyzes the deamination of histidine to urocanate, the initial step of histidine catabolism. Deficiency of the… …   Medical dictionary

  • ammonia-lyase — am·mo·nia ly·ase (ə mōnґyə liґās) [EC 4.3.1] a sub subclass of enzymes of the lyase class that catalyze the formation of a C C bond in a molecule by liberation of ammonia, e.g., histidine ammonia lyase …   Medical dictionary

  • Histidine — NatOrganicBox name=2 amino 3 (3H imidazol 4 yl)propanoic acid synonyms=Imidazole alanine PubChem = 773 CAS = 71 00 1 SMILES = N [C@@H] (Cc1 [nH] cnc1)C(O)=O C=6 | H=9 | N=3 | O=2 mass=155.16 g/molHistidine (abbreviated as His or H) [cite web |… …   Wikipedia

  • histidine — α Amino β (4 imidazolyl)propionic acid; the l isomer is a basic amino acid found in most proteins. It is a nutritionally essential amino acid in mammals. h. ammonia lyase an enzyme catalyzing deamination of l h. to urocanate and ammonia; this… …   Medical dictionary

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  • List of EC numbers (EC 4) — This list contains a list of EC numbers for the fourth group, EC 4, lyases, placed in numerical order as determined by the Nomenclature Committee of the International Union of Biochemistry and Molecular Biology.EC 4.1: Carbon Carbon LyasesEC… …   Wikipedia

  • Amino acid — This article is about the class of chemicals. For the structures and properties of the standard proteinogenic amino acids, see Proteinogenic amino acid. The generic structure of an alpha amino acid in its unionized form …   Wikipedia

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