Globoside

Globoside

A globoside is a type of glycosphingolipid with N-Acetylgalactosamine as the side chain.

The side chain can be cleaved by beta-hexosaminidase. If the enzyme is not functioning correctly, then globosides can accumulate, leading to Sandhoff disease.

External links

*
*


Wikimedia Foundation. 2010.

Игры ⚽ Поможем решить контрольную работу

Look at other dictionaries:

  • Globoside — sind Ceramide mit neutralen Oligosacchariden als Kopfgruppen. Das Globosid Blutgruppen P Antigen ist ein neutrales Glycosphingolipid, das auf den Erythrozyten lokalisiert ist.[1] Es besteht aus P1 , P und Pk Antigenen und bildet einen Rezeptor… …   Deutsch Wikipedia

  • Globoside alpha-N-acetylgalactosaminyltransferase — In enzymology, a globoside alpha N acetylgalactosaminyltransferase (EC number|2.4.1.88) is an enzyme that catalyzes the chemical reaction:UDP N acetyl D galactosamine + N acetyl D galactosaminyl 1,3 D galactosyl 1,4 D galactosyl 1,4 D… …   Wikipedia

  • globoside — (= cytolipin K) Major neutral glycosphingolipid found in kidney and erythrocytes …   Dictionary of molecular biology

  • globoside — A glycosphingolipid; specifically, a ceramide tetrasaccharide (tetraglycosylceramide), isolated from kidney and erythrocytes; accumulates in individuals with Sandhoff disease. * * * glo·bo·side glō bə .sīd n a complex glycolipid that occurs in… …   Medical dictionary

  • globoside — …   Useful english dictionary

  • GBGT1 — Globoside alpha 1,3 N acetylgalactosaminyltransferase 1, also known as GBGT1, is a human gene.cite web | title = Entrez Gene: GBGT1 globoside alpha 1,3 N acetylgalactosaminyltransferase 1| url = http://www.ncbi.nlm.nih.gov/sites/entrez?Db=gene… …   Wikipedia

  • B3GALNT1 — Beta 1,3 N acetylgalactosaminyltransferase 1 (globoside blood group), also known as B3GALNT1, is a human gene.cite web | title = Entrez Gene: B3GALNT1 beta 1,3 N acetylgalactosaminyltransferase 1 (globoside blood group)| url = http://www.ncbi.nlm …   Wikipedia

  • Groupe sanguin — Pour le groupe humoristique québécois, voir Le Groupe sanguin. Un groupe sanguin est une classification de sang reposant sur la présence ou l absence de substance antigéniques héritées à la surface des globules rouges (hématies). Ces antigènes… …   Wikipédia en Français

  • Globósido — Los Globósidos son oligosacáridos de ceramida que contienen dos o más residuos de azúcar, generalmente: galactosa, glucosa y N acetilgalactosamina. Los oligosacáridos de ceramida son compuestos neutros ya que no tienen carga a PH 7 y además no… …   Wikipedia Español

  • Sandhoff disease — Infobox Disease Name = Sandhoff disease Caption = DiseasesDB = 29469 ICD10 = ICD10|E|75|0|e|70 ICD9 = ICD9|330.1 ICDO = OMIM = 268800 MedlinePlus = eMedicineSubj = eMedicineTopic = MeshID = D012497 Sandhoff disease, also called Hexosaminidase A… …   Wikipedia

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”