King-Kopetzky syndrome

King-Kopetzky syndrome

King-Kopetzky syndrome is an auditory disability with appears clinically as a “normal” hearing threshold. It is also known as "obscure auditory dysfunction (OAD)"The role of a family history in King Kopetzky syndrome (Obscure Auditory Dysfunction). Stephens D., Zhao F.Acta Otolaryngol 2000; 120: 197-200.] or "auditory disability with normal hearing (ADN)", The main reported disability is difficulty in hearing speech in the presence of background noise. [http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=14570238&dopt=Abstract PubMed] ] this is in conjunction with the finding of normal hearing test results.

It was found that King Kopetzky syndrome patients will have a worse Social Hearing Handicap index (SHHI),indicating they suffer a significant degree of speech-hearing disability.Determinants of speech-hearing disability in King Kopetzky syndrome. Zhao F, Stephens D. Scand Audiol.1996;25(2):91-6.]

Causes

It seems that somatic anxiety and situations of stress may be determinants of speech-hearing disability.Auditory and psychological factors in ‘auditory disability with normal hearing’. King K, Stephens D. Scand Audiol. 1992;21(2):109-14.]

Some studies indicated an increased prevalence of a family history of hearing impairment in these patients. The pattern of results is suggestive that King-Kopetzky patients may be related to conditions of autosomal dominant inheritance.Audiometric configuration in non-syndromic genetic hearing loss. Liu XZ, Xu L, Newton V. J Audiol Med 3:99-106] Non-syndromic hearing impairment: unparalleled heterogeneity. Van Camp G, Willems PJ, Smith RJH (1997). Am J Genet 60:758-764.]

ubcategories

It was found that based on sensitized measures of auditory dysfunction and on psychological assessment, Subjects could be subdivided into seven subcategories [http://www.medscape.com/medline/abstract/10997453 Zhao F; Stephens D, Subcategories of patient with King-Kopetzky syndrome Br J Audiol .2000;34(4):241-56.] ] .

1- middle ear dysfunction

2- mild cochlear pathology

3- central/medial olivocochlear efferent system (MOCS) auditory dysfunction

4- purely psychological problems

5- multiple auditory pathologies

6- combined auditory dysfunction and psychological problems

7- unknown

Different subgroups may represent different pathogenic and aetiological factors. Thus, subcategorization provides further understanding of the basis of King-Kopetzky syndrome, and hence may guide the rehabilitative management of these patients.

Recent research

There has been some interest in testing that King-Kopetzky syndrome might be an early stage of late onset familial hearing impairment by Professor Dafydd Stephens, F Zhao and Angeles Espeso at the Welsh Hearing Institute, Cardiff University.

ee also

*Hearing impairment
*List of eponymous diseases
*Professor Dafydd Stephens

References


Wikimedia Foundation. 2010.

См. также в других словарях:

  • King-Kopetzky syndrome — see obscure auditory dysfunction …   The new mediacal dictionary

  • Hearing impairment — See also: Deaf culture for the social movement.. Deaf and/or hard of hearing Classification and external resources The International Symbol for Deafness …   Wikipedia

  • List of eponymous diseases — An eponymous disease is one that has been named after the person who first described the condition. This usually involves publishing an article in a respected medical journal. Rarely an eponymous disease may be named after a patient (examples… …   Wikipedia

  • Cocktail party effect — The cocktail party effect describes the ability to focus one s listening attention on a single talker among a mixture of conversations and background noises, ignoring other conversations.[1] The effect enables most people to talk in a noisy place …   Wikipedia

  • Speech perception — is the process by which the sounds of language are heard, interpreted and understood. The study of speech perception is closely linked to the fields of phonetics and phonology in linguistics and cognitive psychology and perception in psychology.… …   Wikipedia

  • obscure auditory dysfunction — OAD; = King Kopetzky syndrome hearing difficulty, especially in noisy environments, in an individual with a normal audiogram. Treatment includes hearing therapy …   The new mediacal dictionary


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