Adiposogenital dystrophy


Adiposogenital dystrophy

Infobox_Disease
Name = PAGENAME


Caption =
DiseasesDB = 29318
ICD10 = ICD10|E|23|6|e|20
ICD9 = ICD9|253.8
ICDO =
OMIM =
MedlinePlus =
eMedicineSubj =
eMedicineTopic =
MeshID =

Adiposogenital dystrophy is a medical condition.

Presentation

It is characterized by:
* Feminine obesity
* Growth retardation and retarded sexual development, atrophy or hypoplasia of the gonads, and altered secondary sex characteristics,
* headaches
* mental retardation, problems with vision
* polyuria, polydipsia.

It is usually associated with tumours of the hypothalamus, causing increased appetite and depressed secretion of gonadotropin. It seems to affect males mostly.

Many overweight children may appear to have the disorder because of the concurrence of obesity and retarded sexual development; these children have no endocrine disturbances, however, and they mature normally after delayed puberty.

ynonyms

It has several other names: [ [http://www.rarediseases.org/search/rdbdetail_abstract.html?disname=Froelich%27s%20Syndrome National Organisation for Rare Disorders - Froelich's syndrome] ]

* "Babinski-Fröhlich syndrome" [WhoNamedIt|synd|1792 - Babinski-Fröchlich syndrome] (named after Joseph Babinski [J. F. Babinski. Tumeur du corps pituitaire sans acromégalie et avec arrêt de développement des organes génitaux. Revue neurologique, Paris, 1900, 8: 531-535. ] and Alfred Fröhlich, [A. Fröhlich. Ein Fall von Tumor der Hypophysis cerebri ohne Akromegalie. Wiener klinische Rundschau, 1901, 15: 833-836; 906-908. ] but probably first described by Morgagni).Fact|date=November 2007 (It was given its name by Harvey Cushing.)cite journal |author=Zárate A, Saucedo R |title= [The adiposogenital distrophy or Frohlich syndrome and the beginning of the concept of neuroendocrinology] |language=Spanish; Castilian |journal=Gac Med Mex |volume=143 |issue=4 |pages=349–50 |year=2007 |pmid=17969845 |doi=]
* "Froelich's syndrome"
* "Frölich's Syndrome"
* "Hypothalamic Infantilism-Obesity"
* "Launois-Cleret Syndrome"
* "Sexual Infantilism"

ee also

* Prader-Willi syndrome, to which it might resemble. However, this is a genetic disorder.

References


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Look at other dictionaries:

  • adiposogenital dystrophy — ad·i·po·so·gen·i·tal dystrophy .ad ə .pō sō .jen ət əl n a combination of obesity, retarded development of the sex glands, and changes in secondary sex characteristics that results from impaired function or disease of the pituitary gland and… …   Medical dictionary

  • adiposogenital dystrophy — ˌadə|pōsō|jenəd.əl noun Etymology: adipose + o + genital : a combination of obesity, retarded development of the sex glands, and changes in secondary sex characteristics that results from impaired function or disease of the pituitary gland and… …   Useful english dictionary

  • dystrophy — Progressive changes that may result from defective nutrition of a tissue or organ. SYN: dystrophia. [dys + G. trophe, nourishment] adiposogenital d. a disorder characterized primarily by obesity and hypogonadotrophic hypogonadism …   Medical dictionary

  • adiposogenital degeneration — see under dystrophy …   Medical dictionary

  • adiposogenital syndrome — see under dystrophy …   Medical dictionary

  • dystrophia adiposogenitalis — adiposogenital dystrophy …   Medical dictionary

  • Babinski-Frцhlich syndrome — adiposogenital dystrophy …   Medical dictionary

  • Frцhlich syndrome — adiposogenital dystrophy …   Medical dictionary

  • syndrome — The aggregate of symptoms and signs associated with any morbid process, and constituting together the picture of the disease. SEE ALSO: disease. [G. s., a running together, tumultuous concourse; (in med.) a concurrence of symptoms, fr. syn,… …   Medical dictionary

  • Androgen insensitivity syndrome — Classification and external resources AIS results when the function of the androgen receptor (AR) is impaired. The AR protein (pictured) mediates the effects of androgens in the human body. ICD 10 E …   Wikipedia